Ukuphazamiseka ekuphuhliseni izicubu ezixhumeneyo kubangela ukuxinwa kwawo kunye nobunzima. Le nqubo ibizwa ngokuba yi-systemic scleroderma kwaye ibonakaliswe ngokutshatyalaliswa ngokukhawuleza kwemithambo encinci yegazi, i-epidermis, kunye nezinye izitho zangaphakathi.
Isifo se-scleroderma
Ngenxa yezizathu ezingaziwa, abafazi bahlushwa ngamaxesha angama-7 ngokuphindaphindiweyo kunamadoda avela kwesi sifo, kwaye i-systemic scleroderma ivela ngokubanzi xa ikhulile.
Esi sifo sibonakala ngentuthuko ephuculweyo kunye nokuguqulwa kokutshintshwa kwezicubu emzimbeni, kwesikhumba ukuya ezintso, intliziyo nemiphunga.
I-scleroderma ye-Systemic
Abanye oogqirha bacacisa ukuba le nto isifo siyashukunyiswa zizifo ezizimelayo kunye neziganeko zokuzalwa. Ukongeza kwezi nguqulelo, ezi zilandelayo zibeka ingozi:
- imisebenzi yobugcisa enxulumene nomsebenzi kwindawo yokusebenzela apho kuvela khona izibilini ezinamandla;
- i-hypothermia rhoqo okanye ixesha elide;
- izifo ezithathelwanayo ezichaphazela inkqubo ye-nervous;
- ukukhubazeka kophuhliso lwama-vascular;
- Ukuhamba kwegazi okwaneleyo kwimizimba.
Iimpawu ze-scleroderma
Inkqubo yekliniki yesi sifo ineempawu ezinjalo:
- uvakalelo lwamaqabunga eminwe yezandla, i-pallor, ukubonakala kweentlungu ezingabonakaliyo ( isifo sikaRaynaud );
- i-edema yemilenze ngokuqina kancinci kwesikhumba kubo;
- ubude buso;
- intlungu kumalungu kunye nezihlunu, ezifana ne-arthritic okanye i-rheumatoid;
- ukuhla kwezandla kunye neenyawo;
- ukuhluleka kwezintso;
- isifo sesifo entliziyweni, emaphaphu, nge-peritoneum;
- ukuphazamiseka kokugaya ukutya, ukuzithemba;
- ukuphefumula okufutshane;
- i-arrhythmia .
Inkqubo ye-scleroderma - ukuxilongwa
Ngenxa yokufana kwezi zimpawu ezichazwe ngentla ngezinye izifo, kunzima ukufumanisa isigulo, kuba kukho ezininzi iintlobo zophando ezifunekayo. Okokuqala, ingqwalasela ifakwe kwiimpawu zangaphandle - i-pallor yesikhumba, ukuguqulwa kwimibala ebusweni (kuba njengobumba obuthile kunye nemilomo emincinci), ubuncinci bezandla kunye neminwe enobumba kunye ne-phalanges yeminwe.
Ukongezelela, uvavanyo olunzulu lwegazi luyenziwa ukuchonga iinkqubo ezivuthayo, i-immunogram, uvavanyo lwe-X-ray lwezitho zangaphakathi ukufumana isantya sesilonda sabo, kunye ne-electrocardiogram.
I-Scleroderma systemic - prognosis
Ngaphandle kokuba kusekwe izizathu ezibalulekileyo zesifo, ayikwazi ukuphiliswa, ngoko ukukhubazeka kuya kuba nzima kwaye ekugqibeleni kubangela ukukhubazeka kwesigulane.
I-scleroderma ye-System inesimo esicacileyo sinokungalindelekanga, isibalo esincinane sezigulane siphatha ixesha elide kuneminyaka emi-2. Ngonyango olufanelekileyo, kunokwenzeka ukuphucisa ukuqhubela phambili kwesi sifo kunye nokunyusa eli xesha ukuya kwiminyaka emi-5-7.
Inkqubo ye-scleroderma yonyango kunye nolwalathiso olutsha kule ntsimi
Ukunciphisa iimpawu kunye nokuphucula umgangatho wobomi bomntu, indlela edibeneyo yokonyango isetyenziswa:
- amalungiselelo antifibrotic;
- amahomoni e-corticosteroid anti-inflammatory;
- yokubuyisela amayeza;
- immunosuppressors;
- I-Physiotherapy (izicelo zezidaka, iibhagi zokuhlamba iipine, iinkqubo zomsakazo womsakazo);
- ukucoca umzimba;
- gymnastics.
Okwangoku, uphando olunzulu kunye novavanyo
Inkqubo ye-scleroderma yonyango kunye nezilwanyana zamalungu
Kwimichiza ehlukile kunconywa ukuba uthathe i-decoctions ye-vasodilating i-herbs-hawthorn, iSt John's wort, i-motherwort, i-oregano, i-burdock, i-clover ne-calendula esikhundleni sethi.
Ukongezelela, i-compress inceda ukunciphisa intlungu evela kumjelo omlilo osisandulisiwe, omele usetyenziswe kwiindawo ezichaphazelekayo imihla ngemizuzu engama-20-30.