Scleroderma

Ukuphazamiseka ekuphuhliseni izicubu ezixhumeneyo kubangela ukuxinwa kwawo kunye nobunzima. Le nqubo ibizwa ngokuba yi-systemic scleroderma kwaye ibonakaliswe ngokutshatyalaliswa ngokukhawuleza kwemithambo encinci yegazi, i-epidermis, kunye nezinye izitho zangaphakathi.

Isifo se-scleroderma

Ngenxa yezizathu ezingaziwa, abafazi bahlushwa ngamaxesha angama-7 ngokuphindaphindiweyo kunamadoda avela kwesi sifo, kwaye i-systemic scleroderma ivela ngokubanzi xa ikhulile.

Esi sifo sibonakala ngentuthuko ephuculweyo kunye nokuguqulwa kokutshintshwa kwezicubu emzimbeni, kwesikhumba ukuya ezintso, intliziyo nemiphunga.

I-scleroderma ye-Systemic

Abanye oogqirha bacacisa ukuba le nto isifo siyashukunyiswa zizifo ezizimelayo kunye neziganeko zokuzalwa. Ukongeza kwezi nguqulelo, ezi zilandelayo zibeka ingozi:

Iimpawu ze-scleroderma

Inkqubo yekliniki yesi sifo ineempawu ezinjalo:

Inkqubo ye-scleroderma - ukuxilongwa

Ngenxa yokufana kwezi zimpawu ezichazwe ngentla ngezinye izifo, kunzima ukufumanisa isigulo, kuba kukho ezininzi iintlobo zophando ezifunekayo. Okokuqala, ingqwalasela ifakwe kwiimpawu zangaphandle - i-pallor yesikhumba, ukuguqulwa kwimibala ebusweni (kuba njengobumba obuthile kunye nemilomo emincinci), ubuncinci bezandla kunye neminwe enobumba kunye ne-phalanges yeminwe.

Ukongezelela, uvavanyo olunzulu lwegazi luyenziwa ukuchonga iinkqubo ezivuthayo, i-immunogram, uvavanyo lwe-X-ray lwezitho zangaphakathi ukufumana isantya sesilonda sabo, kunye ne-electrocardiogram.

I-Scleroderma systemic - prognosis

Ngaphandle kokuba kusekwe izizathu ezibalulekileyo zesifo, ayikwazi ukuphiliswa, ngoko ukukhubazeka kuya kuba nzima kwaye ekugqibeleni kubangela ukukhubazeka kwesigulane.

I-scleroderma ye-System inesimo esicacileyo sinokungalindelekanga, isibalo esincinane sezigulane siphatha ixesha elide kuneminyaka emi-2. Ngonyango olufanelekileyo, kunokwenzeka ukuphucisa ukuqhubela phambili kwesi sifo kunye nokunyusa eli xesha ukuya kwiminyaka emi-5-7.

Inkqubo ye-scleroderma yonyango kunye nolwalathiso olutsha kule ntsimi

Ukunciphisa iimpawu kunye nokuphucula umgangatho wobomi bomntu, indlela edibeneyo yokonyango isetyenziswa:

Okwangoku, uphando olunzulu kunye novavanyo i-stem transplantation ye-cell ukupheliswa ngokupheleleyo kwe-pathology. Iziphumo eziphambili zolu lathiso olutsha lubonisa ukuba olo hlobo unyango kwixesha elizayo luya kunceda ama-95% wezigulane.

Inkqubo ye-scleroderma yonyango kunye nezilwanyana zamalungu

Kwimichiza ehlukile kunconywa ukuba uthathe i-decoctions ye-vasodilating i-herbs-hawthorn, iSt John's wort, i-motherwort, i-oregano, i-burdock, i-clover ne-calendula esikhundleni sethi.

Ukongezelela, i-compress inceda ukunciphisa intlungu evela kumjelo omlilo osisandulisiwe, omele usetyenziswe kwiindawo ezichaphazelekayo imihla ngemizuzu engama-20-30.