Cystic fibrosis kubantwana

I-Cystic fibrosis iyisifo esibuhlungu esichukumisayo esichaphazela zonke iistim zomzimba womntu ovelisa i-mucus-ukuphefumula, ukugaya inyama, isondo, i-sweat glands. Esi sifo siqhelekileyo, kodwa kude kube kutshanje, ukunakekelwa kwengqalelo kwonyango lwawo alukhanga. Izigulane zeCystic fibrosis kufuneka zithole imithi ekhethiweyo ngokufanelekileyo ebomini babo bonke, ziqhube iimviwo rhoqo kwaye ziphathwe ngokusisigxina ngexesha lexesha lokuxhatshazwa.

Isizathu kunye neendlela ze-cystic fibrosis

Isizathu sesifo sisiguqu se-gene cystic fibrosis. Imfuyo yafunyanwa kuphela kwiminyaka engamashumi amathathu edlulileyo. Ukuguqulwa kwesigenjana kubangela ukuba imfihlelo efihliweyo kwiintlanzi ziba nzima kakhulu. Imfihlelo ekhunileyo ihamba ngeengcambu kunye nezicubu, ihlakulela izilwanyana ezincinci - i-Pseudomonas aeruginosa, i-Staphylococcus aureus, intonga ye-hemophilic. Ngenxa yoko, ukuvuvukala okungapheliyo kuqhubeka.

I-cystic fibrosis ivela kwiifom ezintathu:

Iimpawu ze-cystic fibrosis kwiintsana

  1. Isithintelo samathumbu esiswini (i-mekonial ileus) - kumathumbu amancinci ukuxutywa kwamanzi, i-sodium kunye ne-chlorine iyaphazanyiswa, ngenxa yokuba ihlanganiswe ne-meconium. Isisu sithukuthela kumntwana, siphunga nge-bile, isikhumba somekile kwaye siqhekeke, umzekelo we-vascular uvela kwisisu, umntwana uyaba lukhuni kwaye angasebenzi, iimpawu zokuzihlamba zibonakaliswa ngamathole
  2. I-jaundice ehlala ixesha elide - ibonakaliswe kwisiqingatha seemeko ze-ileus ye-meconial, kodwa iphinda isebenze njengesibonakaliso esizimeleyo sesi sifo. Ivela ngenxa yokuba i-bile iba yinyame kakhulu kwaye iphuma kakuhle kwi-gallbladder.
  3. Umntwana ubeka iikristali zetyuwa elukhumbeni ebusweni kunye neengqungquthela, ulusu luba yintyatyambo.

Iimpawu ze-cystic fibrosis kwiintsana

Ngokuqhelekileyo, i-cystic fibrosis ibonakalisa xa usana ludluliselwa kwisondlo esinyanyisiweyo okanye injected foods complementary:

1. Usihlalo uyaqina, atyebile, aninzi kwaye ahlasele.

2. Isibindi sanda.

3. Kukho ukutshabalalisa kwe-rectum.

4. Umntwana ulahla emva kokukhula kwenyama kwaye uhlakulele iimpawu zesifo sokunyuka kwesifo:

5. Kumntwana okhulelweyo uqala ukukhwehlela ixesha elide elingapheliyo. Ubumbano obuninzi buxhamla kwi-bronchi kwaye buphazamisa ukuphefumula okuqhelekileyo. Kwi-mucus eqhubekayo, ibhaktheriya yanda ngokunyanisekileyo, ngenxa yokuba kukho ukuvuvukala kwe-purulent.

Abantwana abane-cystic fibrosis kufuneka bafumane unyango olufanelekileyo. Iinkalo ezinyathelo zokwelapha ziquka:

Ukuhlola iintsana ze-cystic fibrosis

I-Cystic fibrosis inokufunyanwa njengesiphumo seemviwo zonyango kunye nebhubhoratri. Ukuze isifo sifumaneke kwangoko kunokwenzeka, i-cystic fibrosis ifakiwe kwinkqubo yokuhlola abantwana abasandul 'ukuzalwa kunye nezifo ezizalwayo.

Ukuqwalasela umntwana esesibhedlele kuya kuthatha isampuli yegazi (ngokuqhelekileyo isuka kwesithende) ngeendlela "ezomileyo". Oku kwenziwa ngomhla we-4 kubantwana abazalwa ngexesha okanye ngomhla we-7 kwiintsana ezingekafiki. Isampula yegazi isetyenziswe kumgca wokuvavanya, oza kuthi ulandelwe kwisifundo kwibhubhoratri. Ukuba kukho ukukrokra kwe-cystic fibrosis, abazali baxelelwa ngokukhawuleza malunga nemfuneko yoviwo olongezelelweyo.