Hypertrophic cardiomyopathy

Esi sifo, esibangela udonga lwesobunxele, kwaye kwiimeko ezingabonakaliyo ze-ventricle yenhliziyo, kuthiwa yi-hypertrophic cardiomyopathy (HCMC). Esi sifo, ukunyuka kwiimeko ezinqabileyo kakhulu kubonakala ngokulinganayo, kwaye ngoko ke i-septum ye-interventricular ivame ukulimala.

Kukholelwa ukuba esi sisifo sabathathi - kuba kungenxa yokunyuka komzimba okwenyukayo ukuba i-hypertrophy ivela. Sisazi amaqela ambalwa xa abagijimi befa kwimidlalo yezemidlalo ngenxa ye-hypertrophic cardiomyopathy - umdlali webhola waseHungary uMikelos Feher kunye nomdlali wezemidlalo waseMerika uJese Marunde.

Esi sifo, iintambo ze-muscle kwi-myocardium zinendawo ekhuselekileyo, ehambelana nokuguqulwa komzimba.

Iifom ze-hypertrophic cardiomyopathy

Namhlanje, oogqirha bachaza iintlobo ezi-3 ze-cardiomyopathy hypertrophic:

  1. Isithintelo esisiseko - i-gradient ekuphumleni kunkulu okanye ilingana ne-30 mm Hg. Ubugcisa.
  2. Umqobo wokubhaliweyo - ukuguquguquka okuqhelekileyo kwe-gradient intraventricular.
  3. Ukuvinjelwa kweMatriki - i-gradient kwisimo sokuzola ngaphantsi kwama-30 mm Hg. Ubugcisa.

Ukukhusela i-hypertrophic cardiomyopathy ihambelana nale ntlobo yesithathu yesifo, ngelixa ifomu elingenakunqandeka ibonakaliswe ngumgca we-stenosis ngaphantsi kwama-30 mm Hg. Ubugcisa. kwimeko yokuzola kunye nefuthe.

Iimpawu ze-hypertrophic cardiomyopathy

Iimpawu ze-hypertrophic cardiomyopathy zingasekho - malunga ne-30% yezigulane azenzi izikhalazo, apho imeko yokufa ngokukhawuleza ingaba yinto ebonakalayo yeso sifo. Kwindawo ekhethekileyo yobungozi zizigulane ezincinci ezingagcinanga izikhalazo, ngaphandle kokuphazamiseka kwentliziyo.

Kuba esi sifo sibonakala nge-so-called-out infill syndrome - kule meko, ukuphelelwa amandla, ukuphefumula okufutshane kunye nesisu, kunye nokuhlaselwa kwe- angina .

Kwakhona, nge-hypertrophic cardiomyopathy, kukho ukubonakaliswa kwesimo senhliziyo esishiywe kwesokunxele, esinokukhula sibe yintliziyo yokuhluleka kwentliziyo.

Ukungaphumeleli kwisigqi senhliziyo kunokukhokelela ekuphelelweni. Ngokuqhelekileyo ezi zi-extrasystoles ze-ventricular kunye ne-paroxysms ye-tachycardia ye-ventricular.

Kwiimeko ezinqabileyo kakhulu, izigulane zinokuba ne-endocarditis echaphazelayo kunye ne-thromboembolism.

Ukuxilongwa kwe-hypertrophic cardiomyopathy

Ngokungafani nezinye iindidi ze-cardiomyopathy, ifomu le-hypertrophic lifunyaniswa lula kakhulu ngenxa yesigxina esisisiseko: ukuba ukuxilongwa ukuba kuphunyezwe, ukunyuka kwe-myocardial makube mkhulu kunokulingana no-1.5 cm kunye nobukho be-ventricular disysction (ukungaphumeleli okungekhoyo).

Xa uhlolwe, isigulane sifumaneka ukwandisa umngcele wentliziyo ngakwesobunxele, kwaye xa isithintelo, isandi siva (systolic rhomboid).

Phakathi kweendlela ezongezelelweyo zokufunda le nkalo zilandelayo:

Unyango lwe-hypertrophic cardiomyopathy

Ukuxilongwa kunye nokunyangwa kwe-cardiomyopathy ye-hypertrophic ihlobene ngokuthe ngqo ukukhusela isiphumo esibulalayo. Emva kokuvavanya ukugqitywa kwekhosi yesi sifo, ukuba kukho isiphumo esibulalayo, unyango olunzima luyenziwa. Ukuba akukho nengozi yokufa, kwaye iimpawu azikho ziboniswa, ngoko ke unyango olulodwa alukwenziwanga.

Ukunyanga kubaluleke kakhulu ukunciphisa umsebenzi wokwenyama, kunye nokuthatha iziyobisi ngefuthe le-ionotropic. Olu hlobo luquka i-beta-blockers kunye nabaphikisi be-calcium. Zikhethwe ngabanye, kwaye zinikwe ukuba ukwamkelwa okwenziwa ixesha elide (kuze kube yikwamukelwa yonke imihla), oogqirha banamhlanje bazama ukumisela amayeza aneempembelelo ezincinci. Kwakusetyenziswe u-Anaprilin ngaphambili, kwaye namhlanje kuninzi izizukulwana zesizukulwana esitsha.

Kwakhona, imishanguzo yamachiza kunye neyeza-antibiotics zisetyenziselwa unyango xa kukho isifo esithathelwanayo se-pathology.