I-muscular dystonia

Iziphambano zomzimba ezizibandakanya ngokuzenzekelayo kwaye zihamba nezikhundla ezingavumelekanga zengxenye yomzimba, umsebenzi ongenagqirha, onokuthi zichaphazele abantwana, kodwa ziphinde zenzeke kubantu abadala. I-muscular dystonia yintloko okanye idiopathic kwiimeko ezingama-90%. I-10% eseleyo ibhekiselele kwintlobo yesibini yokugula.

Izizathu ze-muscular dystonia syndrome

Ngokuqhelekileyo, isifo esicatshungulwayo kwifom yeprayimali sihlaselwa kwimvelaphi yezinto eziphilayo kwaye siqala ukuqhubela phambili ebuntwaneni.

I-dystonia yesibini inezizathu ezilandelayo:

Iimpawu ze-muscular dystonia kubantu abadala

Impawu zokuqala zesifo ziquka:

Kwixesha elizayo, ezi zilandelayo zibonakaliswa kliniki:

Kubalulekile ukuba uqaphele ukuba isifo esichazwayo sibhekisela kwizifo ezingenakuphilisa kwaye ziyaqhubeka ziqhubeka. Injongo yeempembelelo zokwelapha kukunciphisa iimpawu, ukuphucula umqhubi wemoto kunye nokuxolelwa okuzinzileyo kweentsholongwane.

Unyango lwe-muscular dystonia

Indlela edibeneyo yokuxazulula le ngxaki iquka:

  1. Unyango olusisigxina (unyango). Ixhasa ukulawulwa kwee-dopaminergic, anticholinergic kunye ne-GABAergic iziyobisi ezijoliswe ekuqhelweni kweenkqubo eziqhelekileyo kwi-neurons.
  2. Ukungena kwi-toxin ye-botulinum. Amancinci amancinci alo mzimba we-block block muscle, ukukhusela umzimba ukuba ungathathi izinto ezingaqhelekanga.
  3. Ukuvuselela ngokujulile kwengqondo ngokusebenzisa i-electrodes ezikhethekileyo.
  4. Imizimba ye-Physiotherapy, isethi yokuzivocavoca.
  5. Unyango lwamaxwebhu, ukuhlaziya.