Isifo se-Hirschsprung sisifo seganglion sokuzalwa esithombeni esikhulu samathumbu. Isigulane asinayo iiseliti zesisombululo kwi-plexus ye-Meissner kunye ne-plexus ye-Auerbach. Ngenxa yokungabikho kweziphambano kwiindawo ezichaphazelekayo kunye nokuxilwa kwexesha elide kwamanye amasebe, kukho ukwandisa okwandisa nokwandisa kwamanzi.
Izibonakaliso zesifo seHirschsprung
Iimpawu zokuqala zesifo sikaHirschsprung zizithemba, ukuziqhayisa kunye nokwanda kwinqanaba lesisu. Ukuba isigulane ayibonane nodokotela, izibonakaliso zexesha elide ziqala ukuvela. Ezi ziquka:
- ukukhulelwa kwegazi ;
- hypotrophy;
- ngamatye.
Kwezinye iimeko, izigulane ziva iintlungu kwisisu, amandla abo anganyuka njengoko ixesha lokuqhaqha landa.
Izigaba zeHirschsprung
Isifo seHirschsprung sikhula kwizigaba eziliqela. Isigaba sokuqala sesi sifo sihlawulelwa: isigulane sinokuqhawulwa, kodwa ixesha elide, ukuhlanjululwa okuhlukeneyo kulula ngokukuphelisa.
Emva koko, isigaba esincinci senzeke, ngexesha apho isigulane sesigxina kwaye sithinteke kakhulu. Kule nqanaba ekuphuhlisweni kwesifo sikaHirschsprung kubantu abadala, ubunzima bomzimba buncipha, baxhalabisayo ubunzima besisu kunye nokuphefumula okufutshane. Kwezinye iimeko, ukuphazamiseka kwegazi kunye nokuphazamiseka kwemizimba kubonakala.
Isigaba esilandelayo sesi sifo siyahlawulwa. Izigulane azisincediswa ngokucoca i-lames and various laxatives. Usenomvakalelo wesisu esiswini esezantsi, kwaye isithintelo esiswini siphuthuma ngokukhawuleza.
Ukuxilongwa kwesifo seHirschsprung
Xa kunokukrokrelwa kwesifo seHirschsprung, uviwo lwama-rectal luqhutywa kuqala. Ngaphambi kwesi sifo, i-ampoule engenalutho ye-rectum ifumaneka kwisigulane. I-tone ye-sphincter yanda. Kule meko, kuyimfuneko ukuba uqhube uphando lwe-radiography yazo zonke iziko zesisu esiswini. Ngesifo sikaHirschsprung, izikhonkwane zekoloni zandisiwe kwaye zihluthe, ngamanye amaxesha zibona amanqanaba amanzi.
Isigulana sidinga nokuba nesigmoidoscopy, irrigography, colonoscopy kunye ne-histochemical diagnostics.
Ukunyangwa kwesifo sikaHirschsprung
Indlela yonyango yokuphatha isifo sikaHirschsprung utyando. Iinjongo eziphambili zomsebenzi zi:
- ukucinywa kwamanqanaba onke;
- ukususwa kwe-aganglionic zone;
- ukulondolozwa kwengxenye yamathumbu amakhulu asebenzayo.
Kuyabantwana, imisebenzi yaseSweden, iDuhamel kunye neSoave yenzeke. Abadala ukusebenza kwabo kwifomu eqhelekileyo kuyaphikisana ngenxa yeempawu zobunzima kunye ne-sclerosis enzima kwiimfomula okanye ezincinci zamathumbu. Ngokuqhelekileyo, ngesifo sikaHirschsprung, ukusebenza kukaDuhamel kuguqulwa, apho ummandla we-aganglionary ususwe kunye nokudala isikhephe esifutshane se-rectum. Kwiimeko ezininzi, kunokwenzeka ukukhusela umonakalo kwi-sphincter ye-anus kwaye wenze i-anastomosis e-colorectal.
Ngaphambi kokuhlinzwa, isigulane sidinga
Isalathiso esipheleleyo sesifo sikaHirschsprung emva kokuhlinzwa siyancomeka. Kodwa kwezinye iimeko, ukuhlinzwa ngokuphindaphindiweyo kunokufuneka. Phantse njalo iinjongo zokusebenza okunjalo zinciphisa ukuhlaziywa kwakhona kwe-anastomosis kwaye iqhutyelwa nge-peritoneal okanye i-perinal access.