Isifo sezintso zePolycystic sisifo esibonakaliswe ngumbono wezintso zezintso zamanqwanqwa amaninzi ahlukeneyo, anamaqhekeza angamaqhekeza amancinci athathwe kwi-capsule kwaye azaliswe ngento ekhoyo. Kule nxu lumano, iinkqubo zokwenziwa komchamo kunye nokukhutshwa kwemveliso yerkunkuma evela kumzimba ziphulwa.
Izizathu zesifo sezintso ze-polycystic
Kuye kwaqinisekiswa ngokuqinisekileyo ukuba lesi sifo sinezifo zofuzo, ezixhunyaniswe nokuguqulwa kwamagciwane athile azuzwe kumnye wabazali. Kwaye amabhinqa namadoda anelungelo lokukhubazeka.
I-Pathogenesis kunye neempawu ze-polycystic isifo sesifo
Kwiimeko ezininzi, ukubonakaliswa kokuqala kwesi sifo kubonakala phakathi okanye ubudala, kwaye ngaphambi kweli xesha i-polycystosis iyaqhubeka ingenakuqonda, iyaqhubeka ihamba phambili. Kukho ukwanda kobukhulu kunye nobunzima beentliziyo zombini, ezikulo mzekelo zifumana ubuninzi obunobunzima bomhlaba. Iindonga zee-cysts ziqukethe iisisombululo ezixhamlayo, kwaye ngaphakathi ngaphakathi kwendawo yazo zihlanganiswe ne-flat or cubic epithelium. Umkhuhlane ozalisa i-cysts isondele ngokubumba kumchamo, unombala ophuzi okanye obomvu.
Iziza zeentso zeengtso eziphakathi kwamakhredithi ngamnye ziyakuthatyathwa ngabo kwaye zixhomekeke kwimitshintsho ye-dystrophic, ukungabikho kwegazi kunye ne-atrophy. Ngesi sifo, i-kidney calyces kunye ne-pelvis iyakwandisa ubukhulu, i-deform. Kwezinye iimeko, ii-cysts ezixhasayo. Ngokubhekiselele ekunciphiseni kwempumelelo kwigazi, iimveliso ezinokuqhelanisa ziqala ukuqokelela, ezingagqithwanga emzimbeni kwaye zityhefu.
Kukho izigaba ezintathu zentsholongwane, ezibonakaliswe ziimpawu ezilandelayo:
1. Inqanaba lokuhlawula:
- iintlungu ezibuhlungu okanye ezibuhlungu kwindawo yengqondo;
- ubuthathaka, ukukhathala;
- ubuhlungu obuvela rhoqo kwiintloko.
2. Isigaba senkxaso:
- umlomo owomileyo ;
- ukoma njalo;
- ukuhlaselwa yesohlunu nokuhlanza;
- kunyusa uxinzelelo lwegazi;
- intloko;
- intlungu ebuhlungu kwiindawo zeengtso;
- ukwandiswa komchamo.
3. Isigaba se-compensation:
- ukuwohloka okukhulu kwintlalo-ntle;
- ukuphika isisulu kunye nokuhlanza;
- izibonakaliso zokusuleleka kumathambo;
- igazi kumchamo;
- i-palpation ebonakalayo ebonakalayo yeentso, ukunyamezela kwabo.
Ukuxilongwa kwezifo zesifo se-polycystic
Indlela ephumelelayo yokuxilonga i-kidcycystic isifo i-ultrasound. Kwakhona, esi sifo sinokufunyanwa ngezinye iindlela zokwenza izinto:
- I-MRI kunye ne-CT yeentso;
- utywala o
- nephroscintigraphy;
- i-angiography,
Ukumisela umgangatho wembuyekezo yemisebenzi yeentso, iimvavanyo ezizodwa zemigodi negazi zenziwa.
Indlela yokuphatha isifo sezintso ze-polycystic?
Ngelishwa, iyeza zanamhlanje alisakwazi ukuyeka le nkqubo yokugula, ebangelwa utshintsho lwezityalo. Ngoko ke, isiseko sokonyango kwezifo zesifo se-polycystic sisifo sengqondo esibangelwa iziyobisi kunye nokusetyenziswa kweziyobisi kumaqela alandelayo:
- i-anesthetics;
- i antibiotics;
- diuretics ;
- iziyobisi,
Izigulane zikwacetyiswa ukuba zilandele i-calori ephezulu, ukutya okunobuthi nge-vitamin kunye neprotheni, i-fat, ity restriction, ngaphandle kokutya kwe-caffeine, ukutya okwaneleyo kwamanzi. Kwakhona, kufuneka ubale ukunyuka komzimba, imikhwa emibi.
Ama-cysts amakhulu anokucinywa ngamapcctures angama-percutaneous ngaphantsi kolawulo lwe-ultrasound. Xa kukho iingxaki ezinzulu, ukukhutshwa kwezintso kunye nokufakelwa kwethambo kuphakanyisiwe. Ukungaphumeleli kwetyhuna kudinga i-hemodialysis.
Kukho iindlela ezininzi zokuphatha esi sifo, ezininzi zazo ezisekelwe ekungeneni kwangaphakathi kweziyobisi ezisekelwe kwizityalo zonyango. Imimiselo yabantu ihlose ukucoca igazi, ukuphelisa ukuvuvukala kwindlela yokucoca, ukukhusela umkhuhlane, ukunciphisa uxinzelelo lwegazi, njl.
Izindlela zokonyango kwee-polycystic izinso zonyango ziquka ukusetyenziswa kwamanzi e-turpentine, okukhuthaza ukuxutywa komzimba ngokufanelekileyo, ukunciphisa uxinzelelo lwegazi, ukubuyisela isondlo sezintso. Zilungiselelwe ngesiseko se-turpentine emulsion, enokufumaneka kwii-pharmacy.