Ngenxa yezizathu ezingachazwanga, i-bile ducts inokutshatyalaliswa kokunciphisa okulandelayo, okukhokelela ekuxininiseni okungapheliyo kwe-bile. Le ngqungquthela, i-primary sclerosing cholangitis, ihlolwe njengesimo isifo sokuzimela, njengoko ihlala ihamba kunye nezifo ezifana nesifo sikashukela, i- ulcerative colitis , thyroiditis.
Iimpawu ze-sclerosing cholangitis
Ukuchonga i-syndrome echazwe kumanyathelo okuqala akunakwenzeka, kuba iyaqhubeka ixesha elide ngaphandle kweempawu ezibonakalayo. Umfanekiso wekliniki ubonakaliswe ngethuba lophuhliso lwe-cirrhosis yesibindi okanye i-portal hypertension:
- ukhathala okwandisiweyo;
- ukubetha;
- ukunyuka komzimba;
- intlungu kunye nobunzima kwi-hypochondrium efanelekileyo;
- ukuqhelana ngeziqhamo zesikhumba (i-jaundice esesigxina);
- ukuphazamiseka kokutya;
- nqabile - ngumkhuhlane.
Ukuxilongwa kwe-primary sclerosing cholangitis
Ukuqinisekiswa kokusola kwesifo esicatshulwayo, ngaphezu kokuqokelela imbali kunye noviwo lweklinikhi, lwenziwa ngoncedo lwezi zixhobo ezilandelayo kunye nezifundo zelabhoratri:
- i-biochemical, analysis of immunological blood;
- cholangiography;
- biopsy yesibindi;
- ukuvakala komculo;
- elastography yesibindi;
- ukubuyisela kwakhona i-pancreatocholangiography;
- KWIINTLOKO.
Unyango lwe-sclerosing cholangitis
Ukuphulukiswa ngokupheleleyo kwe-pathology akunakwenzeka, unyango lweziyobisi lujolise ekunciphiseni ukuqhubela phambili kwe-cholangitis nokuphucula imeko yesigulane. Iquka izibisi ezilandelayo:
- antispasmodics;
- ihomoni ze-glucocorticosteroid;
- immunosuppressors;
- ze-antifibrogenic;
- i-enzymes yokugaya;
- i-hepatoprotectors ;
- iziyobisi ezisusela kwi-ursodeoxycholic acid.
Ukongeza, i-antihistamines inokucetyiswa ukuba inciphise i-pruritus.
Xa kuthengiswa i-bile ducts kunye nokungahambi kakuhle kwonyango olulondolozayo, utyando olwenzelwe ukufakelwa kwesibindi luyalelwe.